Omphalocele repair corrects a congenital defect in which all or parts of the small intestine, liver, and large intestine are on the outside of the abdomen and enclosed in a membranous sac at birth. This procedure is similar to gastroschisis repair . Omphalocele is an abdominal wall defect in which the intestines and other tissues protrude through a sac at the base of the umbilical cord (umbilicus). This condition is frequently associated with other birth defects, such as heart defects, imperforate anus , urinary problems, and genetic defects. Omphalocele is similar to gastroschisis , except that the organs are enclosed in a sac. Gastroschisis and omphalocele are frequently diagnosed before birth by ultrasound examinations.